Results of a controlled fast in a 7 year old with VLCADD deficiency
| Time | Glucose (mmol/L) | Lactate (mmol/L) | Free fatty acids(µmol/L) | 3-Hydroxybutyrate (µmol/L) |
|---|---|---|---|---|
| Baseline | 6.4 | 1.5 | 489 | <50 |
| 1 hour | 5.2 | 1.0 | ||
| 1 hour 30 min | 5.0 | 0.8 | ||
| 2 hours | 4.8 | 0.7 | ||
| 2 hours 30 min | 4.4 | 0.6 | 361 | 58 |
| 3 hours | 4.6 | 0.7 | 544 | 211 |
| 3 hours 30 min | 4.9 | 0.9 | 577 | 160 |
| 4 hours | 4.9 | 0.8 | 1015 | 96 |
| 4 hours 30 min | 4.8 | 0.7 | 1071 | 94 |
| 5 hours | 4.8 | 0.7 | 1370 | 87 |
VLCADD, very long chain acyl-CoA dehydrogenase deficiency.