Revised diagnostic classification of pulmonary hypertension (2003)
| • Pulmonary artery hypertension (PAH) | |
| Idiopathic PAH | |
| Familial PAH | |
| Related to: | Collagen vascular disease |
| Congenital systemic to pulmonary shunts | |
| Portal hypertension | |
| HIV infection | |
| Drugs and toxins | |
| Others | |
| Associated with significant venous or capillary involvement | |
| Pulmonary veno-occlusive disease | |
| Pulmonary capillary haemangiomatosis | |
| • Pulmonary hypertension with left heart disease | |
| • Pulmonary hypertension associated with lung disease and/or hypoxaemia | |
| • Pulmonary hypertension caused by chronic thrombotic or embolic disease | |
| • Miscellaneous | |