Table 5

Results from a controlled fast in a 9-month-old with glycogen storage disease type 1

TimeLab glucose
(mmol/L)
Bedside glucose
(mmol/L)
Lactate (mmol/L)Free fatty acids (µmol/L)3-Hydroxybutyrate
(µmol/L)
Baseline4.94.82.2111<50
30 min4.24.61.6126<50
60 min4.14.41.1143<50
90 min4.04.01.7180<50
2 hours3.23.41.8291<50
2 hours 15 min2.73.03.2573<50
2 hours 30 min2.93.21.7350<50
2 hours 45 min2.52.81.9308<50